Longitudinal Characterization of the Microbiological Status in Primary Ciliary Dyskinesia: An Italian Multicentre Study
V. Ferraro
Valentina Tonazzo
A. Pandolfo
Claudia Biondi
Alessandra Boni
Melissa Borrelli
C. Calogero
Alberta Circiello
A. Corcione
R. Cutrera
Valentina Fainardi
G. Parisi
M. F. Patria
G. Scopelliti
N. Ullmann
Silvia Carraro
Medicine
Abstract
Primary Ciliary Dyskinesia (PCD) is a genetic disorder characterized by respiratory infections leading to chronic airway colonization and progressive lung damage. The aim of this study is to evaluate prevalence and longitudinal changes of respiratory microbiological profile in children and young adults with PCD, and their association with clinical, functional, and radiological features.