Open access
Aug 2026
An Adamts2 Knock-In Model of Dermatosparaxis Ehlers–Danlos Syndrome Reveals Defective Collagen Maturation
The knock-in Adamts2 mouse model provides a translational platform for studying dEDS pathogenesis and strategies to restore ECM homeostasis and disrupted tissue-wide cellular communication.
Taylor Petrucci-Nelson, A. Weintraub, Matthew Huff et al.
· Biomedicines · 0 citations